SP GA1 C

SP GA1-C: Lysine, Tryptophan Free Formula for Children above 2 years, for the management of Glutaric Acidemia Type 1 (GA1). It’s a blend of essential and nonessential amino acids with carbohydrate, fat, vitamins, minerals, trace elements without amino acids lysine and tryptophan

Use under medical supervision

NOT FOR MEDICINAL USE. 

Not to exceed recommended daily usage 

Product is not to be used as a substitute for varied diet

Store out of reach of children

Description

• “SP GA1-C” a protein substitute containing essential & nonessential amino acids 
• Free from lysine and tryptophan
• Provides carbohydrate, fat, vitamins, minerals and trace elements 
• Choline – a nutrient similar to B vitamins plays a crucial role in brain health for individuals 

Suitable for above 2 years of age

Indications

• For the use of dietary management of proven cases of Glutaric Acidemia for above 2 years of age 
• Can be used in other conditions where restriction of amino acids lysine, or tryptophan or both is indicated. 
• For enteral use only 
• Not for parenteral use
• Not Suitable for Infants 
• Nonsterile formula
• “Nutritionally Incomplete with a standard formulation or nutrient adopted formulation specific for a disease, disorder or medical condition, which is not suitable to be used as sole source of nourishment”.

Dosage 

• To be determined by the Clinician/Dietician. 
• Dose is dependent on age, body weight, complications of the disorder if any and medical condition of the patient
•  ‘Not to exceed the recommended daily usage’.

Direction for Preparation

• The child’s health depends on carefully following the instructions. Proper hygiene, preparation, dilution, use and storage are important when preparing the formula. Failure to follow these instructions could result in severe harm. 
• SP GA1-C Formula should be mixed with calculated amounts of drinks like water, fruit juices; fruits purees, etc. or as suggested by the Clinician/Dietician. If using water to prepare the formula you need to use boiled cooled, water. 
• Use boiled clean utensils, bottles and nipples in water before use. Pour the required amount of water into the bottle/utensil. 
• Add the correct amount of SP formula powder, cap the bottle or cover the utensil and shake vigorously for some time. 
• IF YOU FIND FORMULA IS NOT DISSOLVING PROPERLY THEN TAKE A MEASURED FORMULA IN BOTTLE OR UTENSIL ADD LITTLE LIQUID TO MAKE A PASTE. IF CHILD CAN TAKE THAT MUCH THICK FORMULA, THEN FEED IT AND THEN GIVE REMAINING MEASURED JUICE OR WATER. IF UNABLE TO TAKE PASTE, THEN ADD REMAINING CALCULATED FLUID. SHAKE WELL. 
• If instructed to use the scoop unpacked and use a levelled scoop. 
• Once prepared, product can spoil quickly. Either feed immediately or after feeding begins, use within 1 hour otherwise discard. Do not freeze prepared product. 

Important Notice 

• Should not be boiled nor added to hot food & if wish can give only at lukewarm temperature.

Storage

Unopened: SP GA1-C nutrition formula should be stored in a cool dry place below 25 °C. 

• Always store DRY scoop in a container. 
• Open only one sachet at a time for use. 
• Seal properly after the use
• Once opened: Use within one month. 

Ingredients: Maltodextrin, Dextrose Anhydrous, MCT Fat Powder, L-Alanine, L-Arginine, L-Aspartic acid, L-Cysteine, L-Glutamic Acid, Glycine, L-Histidine, L-Isoleucine, L-Leucine, L-Methionine, L-Phenylalanine, L-Proline, L-Serine, L-Threonine, L-Tyrosine, L-Valine, L-Carnitine, Taurine, L-Glutamine, L-Ornithine, Vitamin A palmitate, Ergocalciferol, Alpha tocopherol, Thiamine hcl, Riboflavin, Niacinamide, Pyridoxine Hcl, Cyanocobalamine, Pantothenic Acid, Folic Acid, Ascorbic Acid, Biotin, vitamin K1, Ferric pyrophosphate, Sodium Chloride, Potassium Chloride, Di Calcium Phosphate, Carbonate, mono potassium Phosphate, Magnesium Oxide, Manganese Sulphate, Potassium Iodide, Sodium Salenite, Copper sulphate, Zinc oxide, Choline bitartarate,

Nutritional Information

SP GA1-C Children Formula
Nutrients*	Unit	Per 100g	Per scoop (8g)	% RDA
Calories		408	33
Protein Equivalent**	g	38.05	3.04
MCT fat g	g	10.4	0.83
Saturated Fat	g	10.4	0.8
Trans fat	g	0	0.00
Total Carbohydrate	g	40.47	3.24
Dextrose	g	16.19	1.30
Amino Acids
L-Leucine	g	5.44	0.43	85.47%
L-Glutamine	g	4.38	0.35	–
L-Arginine	g	4.00	0.32	–
L-proline	g	3.66	0.29	–
L-Glutamic Acid	g	3.34	0.27	–
L-Isoleucine	g	3.27	0.26	96.89%
L-Aspartic acid	g	3.13	0.25	–
L-Tyrosine	g	2.80	0.22	–
L-phenylalanine	g	2.57	0.21	–
Glycine	g	2.33	0.19	–
L-serine	g	1.53	0.12	–
L-Carnitine	g	1.80	0.14	–
L-Alanine	g	1.79	0.14	–
L-Cystine	g	1.07	0.09	96.89%
L-Histidine	g	1.61	0.13	93.02%
L-Methionine	g	1.12	0.09	69.76%
L-Ornithine	g	0.92	0.07	–
L-Valine	g	0.47	0.04	11.92%
L-threonine	g	0.30	0.02	10.35%
Taurine	g	0.13	0.01	–
Minerals
Chloride	mg	1500.0	120.0	5.33%
Calcium	mg	500.0	40.0	8%
Phosphorous	mg	500.0	40.0	4%
Potassium	mg	500.0	40.0	1.14%
Sodium	mg	500.0	40.0	5.33%
Choline	mg	150.0	12.0	–
Magnesium	mg	90.0	7.2	8%
Iron	mg	8.0	0.6	8%
Zinc	mg	3.3	0.3	7.87%
Copper	mg	1.7	0.1	8.23%
Manganese	mg	1.0	0.1	2%
Selenium	mcg	40.0	3.2	8%
Chromium	mcg	25.0	2.0	4%
Iodine	mcg	20.0	1.6	1.77%
Vitamins			0.0
Vitamin C	mg	30.0	2.4	8%
Vitamin E	mg	7.5	0.6	6%
Niacin	mg	7.0	0.6	8%
Pantothenic Acid	mg	1.2	0.1	2.50%
Riboflavin	mg	1.1	0.1	8.18%
Vitamin B6	mg	0.9	0.1	8.57%
Thiamine	mg	0.7	0.1	7.77%
Vitamin A RE	mcg	390.0	31.2	8%
Folic Acid	mcg	70.6	5.6	8%
Vitamin K1	mcg	50.0	4.0	7.27%
Biotin	mcg	20.0	1.6	8%
Vitamin D	mcg	15.0	1.2	8%
Vitamin B12	mcg	1.2	0.1	8%
–	RDA not established

* Product nutrient values and ingredients are subject to change. Please see product label for current information.

** Protein is incomplete since it does not contain the essential amino acids Lysine and Tryptophan. 

Please take ALA and DHA supplement separately